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A50 Congenital syphilis

ICD-10-CM category A50 sits in Chapter 1 (Certain infectious and parasitic diseases, A00-B99). It contains 33 billable codes for FY2027, effective October 1, 2026 to September 30, 2027. Always code to the most specific code available: a code with more characters that describes the diagnosis more precisely takes priority over a shorter one.

Subcategories

A50.0 Early congenital syphilis, symptomaticA50.3 Late congenital syphilitic oculopathyA50.4 Late congenital neurosyphilis [juvenile neurosyphilis]A50.5 Other late congenital syphilis, symptomatic

Billable codes in A50

CodeDescription
A50.01Early congenital syphilitic oculopathy
A50.02Early congenital syphilitic osteochondropathy
A50.03Early congenital syphilitic pharyngitis
A50.04Early congenital syphilitic pneumonia
A50.05Early congenital syphilitic rhinitis
A50.06Early cutaneous congenital syphilis
A50.07Early mucocutaneous congenital syphilis
A50.08Early visceral congenital syphilis
A50.09Other early congenital syphilis, symptomatic
A50.1Early congenital syphilis, latent
A50.2Early congenital syphilis, unspecified
A50.30Late congenital syphilitic oculopathy, unspecified
A50.31Late congenital syphilitic interstitial keratitis
A50.32Late congenital syphilitic chorioretinitis
A50.39Other late congenital syphilitic oculopathy
A50.40Late congenital neurosyphilis, unspecified
A50.41Late congenital syphilitic meningitis
A50.42Late congenital syphilitic encephalitis
A50.43Late congenital syphilitic polyneuropathy
A50.44Late congenital syphilitic optic nerve atrophy
A50.45Juvenile general paresis
A50.49Other late congenital neurosyphilis
A50.51Clutton's joints
A50.52Hutchinson's teeth
A50.53Hutchinson's triad
A50.54Late congenital cardiovascular syphilis
A50.55Late congenital syphilitic arthropathy
A50.56Late congenital syphilitic osteochondropathy
A50.57Syphilitic saddle nose
A50.59Other late congenital syphilis, symptomatic
A50.6Late congenital syphilis, latent
A50.7Late congenital syphilis, unspecified
A50.9Congenital syphilis, unspecified

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