D89 Oth disorders involving the immune mechanism, NEC
ICD-10-CM category D89 sits in Chapter 3 (Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism, D50-D89). It contains 24 billable codes for FY2027, effective October 1, 2026 to September 30, 2027. Always code to the most specific code available: a code with more characters that describes the diagnosis more precisely takes priority over a shorter one.
Subcategories
D89.4 Mast cell activation syndrome and related disordersD89.8 Oth disrd involving the immune mechanism, NECD89.81 Graft-versus-host diseaseD89.83 Cytokine release syndrome
Billable codes in D89
| Code | Description |
|---|---|
D89.0 | Polyclonal hypergammaglobulinemia |
D89.1 | Cryoglobulinemia |
D89.2 | Hypergammaglobulinemia, unspecified |
D89.3 | Immune reconstitution syndrome |
D89.40 | Mast cell activation, unspecified |
D89.41 | Monoclonal mast cell activation syndrome |
D89.42 | Idiopathic mast cell activation syndrome |
D89.43 | Secondary mast cell activation |
D89.44 | Hereditary alpha tryptasemia |
D89.49 | Other mast cell activation disorder |
D89.810 | Acute graft-versus-host disease |
D89.811 | Chronic graft-versus-host disease |
D89.812 | Acute on chronic graft-versus-host disease |
D89.813 | Graft-versus-host disease, unspecified |
D89.82 | Autoimmune lymphoproliferative syndrome [ALPS] |
D89.831 | Cytokine release syndrome, grade 1 |
D89.832 | Cytokine release syndrome, grade 2 |
D89.833 | Cytokine release syndrome, grade 3 |
D89.834 | Cytokine release syndrome, grade 4 |
D89.835 | Cytokine release syndrome, grade 5 |
D89.839 | Cytokine release syndrome, grade unspecified |
D89.84 | IgG4-related disease |
D89.89 | Other specified disorders involving the immune mechanism, not elsewhere classified |
D89.9 | Disorder involving the immune mechanism, unspecified |
Search within ICD-10-CM for D89 and related codes
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