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E75 Disord of sphingolipid metab and oth lipid storage disorders

ICD-10-CM category E75 sits in Chapter 4 (Endocrine, nutritional and metabolic diseases, E00-E89). It contains 26 billable codes for FY2027, effective October 1, 2026 to September 30, 2027. Always code to the most specific code available: a code with more characters that describes the diagnosis more precisely takes priority over a shorter one.

Subcategories

E75.0 GM2 gangliosidosisE75.1 Other and unspecified gangliosidosisE75.2 Other sphingolipidosisE75.24 Niemann-Pick disease

Billable codes in E75

CodeDescription
E75.00GM2 gangliosidosis, unspecified
E75.01Sandhoff disease
E75.02Tay-Sachs disease
E75.09Other GM2 gangliosidosis
E75.10Unspecified gangliosidosis
E75.11Mucolipidosis IV
E75.19Other gangliosidosis
E75.21Fabry (-Anderson) disease
E75.22Gaucher disease
E75.23Krabbe disease
E75.240Niemann-Pick disease type A
E75.241Niemann-Pick disease type B
E75.242Niemann-Pick disease type C
E75.243Niemann-Pick disease type D
E75.244Niemann-Pick disease type A/B
E75.248Other Niemann-Pick disease
E75.249Niemann-Pick disease, unspecified
E75.25Metachromatic leukodystrophy
E75.26Sulfatase deficiency
E75.27Pelizaeus-Merzbacher disease
E75.28Canavan disease
E75.29Other sphingolipidosis
E75.3Sphingolipidosis, unspecified
E75.4Neuronal ceroid lipofuscinosis
E75.5Other lipid storage disorders
E75.6Lipid storage disorder, unspecified

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