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E78 Disorders of lipoprotein metabolism and other lipidemias

ICD-10-CM category E78 sits in Chapter 4 (Endocrine, nutritional and metabolic diseases, E00-E89). It contains 18 billable codes for FY2027, effective October 1, 2026 to September 30, 2027. Always code to the most specific code available: a code with more characters that describes the diagnosis more precisely takes priority over a shorter one.

Subcategories

E78.0 Pure hypercholesterolemiaE78.01 Familial hypercholesterolemiaE78.4 Other hyperlipidemiaE78.7 Disorders of bile acid and cholesterol metabolismE78.8 Other disorders of lipoprotein metabolism

Billable codes in E78

CodeDescription
E78.00Pure hypercholesterolemia, unspecified
E78.010Homozygous familial hypercholesterolemia [HoFH]
E78.011Heterozygous familial hypercholesterolemia [HeFH]
E78.019Familial hypercholesterolemia, unspecified
E78.1Pure hyperglyceridemia
E78.2Mixed hyperlipidemia
E78.3Hyperchylomicronemia
E78.41Elevated Lipoprotein(a)
E78.49Other hyperlipidemia
E78.5Hyperlipidemia, unspecified
E78.6Lipoprotein deficiency
E78.70Disorder of bile acid and cholesterol metabolism, unspecified
E78.71Barth syndrome
E78.72Smith-Lemli-Opitz syndrome
E78.79Other disorders of bile acid and cholesterol metabolism
E78.81Lipoid dermatoarthritis
E78.89Other lipoprotein metabolism disorders
E78.9Disorder of lipoprotein metabolism, unspecified

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