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Q91 Trisomy 18 and Trisomy 13

ICD-10-CM category Q91 sits in Chapter 17 (Congenital malformations, deformations and chromosomal abnormalities, Q00-Q99). It contains 8 billable codes for FY2027, effective October 1, 2026 to September 30, 2027. Always code to the most specific code available: a code with more characters that describes the diagnosis more precisely takes priority over a shorter one.

Billable codes in Q91

CodeDescription
Q91.0Trisomy 18, nonmosaicism (meiotic nondisjunction)
Q91.1Trisomy 18, mosaicism (mitotic nondisjunction)
Q91.2Trisomy 18, translocation
Q91.3Trisomy 18, unspecified
Q91.4Trisomy 13, nonmosaicism (meiotic nondisjunction)
Q91.5Trisomy 13, mosaicism (mitotic nondisjunction)
Q91.6Trisomy 13, translocation
Q91.7Trisomy 13, unspecified

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